摘要
总结1例肝糖原累积症患者肝移植术后继发腹腔出血及脑出血的护理经验。护理要点包括：术前预警低血糖的发生，为手术创造条件，术后警惕高血糖，维持血糖稳定；早期识别腹腔出血，快速响应抢救流程；明确癫痫发作的病因，有效控制脑出血；精细化监测凝血功能，预防再次出血及血栓形成；动态化营养支持，改善患者营养状况。经积极的治疗和护理，患者术后第47天康复出院，随访6个月，恢复良好。
关键词： 肝糖原累积症；肝移植；腹腔出血；脑出血；护理
Abstract
To summarize the nursing experience for a patient with hepatic glycogen storage disease complicated by secondary intra-abdominal hemorrhage and cerebral hemorrhage after liver transplantation. The key points of nursing include: warning of hypoglycemia before surgery to create favorable conditions for the operation; being vigilant of hyperglycemia after surgery to maintain stable blood sugar levels; early identification of abdominal hemorrhage and rapid response to the rescue process; clarifying the cause of epileptic seizures and effectively controlling cerebral hemorrhage; meticulous monitoring of coagulation function to prevent rebleeding and thrombosis; dynamic nutritional support care to improve the patient's nutritional status. Through active treatment and nursing, the patient recovered and was discharged 47 days after the operation. Follow-up for 6 months showed good recovery.
Key words： Hepatic glycogen storage disease; Liver transplantation; Intra-abdominal hemorrhage; Cerebral hemorrhage; Nursing care
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